Saturday, March 23, 2013

Cataracts In Children


Cataracts In Children

Causes and Associated Conditions 

Intrauterine Infection

Rubella
Toxoplasmosis
Herpes simplex
Cytomegalovirus
Varicella


Metabolic Disorders
Galactosemia
Galactokinase deficiency

Hypoparathyroidism
Pseudohypoparathyroidism

Diabetes mellitus
Hypoglycemia

Hyperalimentation (vacuoles)
Mannosidosis

Drug-induced
Cortiocosteroids
Chlorpromazine
Ergot
Naphthalene
Triparanol

Inflammatory
Juvenile rheumatoid arthritis
Sarcoidosis

Atopic dermatitis
Trauma

Genetic/Syndromes
Autosomal dominant
Autosomal recessive
X-linked recessive


Down syndrome (trisomy 21)
Trisomy 13
Trisomy 18
Lowe syndrome
Dubovitz syndrome
Hallerman-Streiff syndrome
Alport’s syndrome
Cri du chat syndrome
Cerebrotendinous xanthomatosis
Marinesco-Sjögren syndrome
Myotonic dystrophy
Rothmund-Thomson syndrome
Cockayne’s syndrome
Incontinentia pigmenti
Stickler syndrome
Craniofacial syndromes
Zellweger syndrome
Wilson’s syndrome
Hallgren syndrome
Laurence-Moon-Bardet-Biedl syndrome
Chondrodysplasia punctata
Refsum’s disease
Congenital ichthyosis

Sclerodactyly
G-6-PD deficiency
Rubinstein-Taybi syndrome

Radiation Injury

Ocular Disease
Retinitis pigmentosa
Aniridia

Persistent Hyperplastic  Primary vitreous
Leber’s congenital amaurosis
Retinopathy of prematurity
Retinoblastoma


s i� $ o r @�� (y� >
dopamine, epinephrine, and dobutamine
            improve cardiac contractility
            increase heart rate
            increase cardiac output.

Digoxin should be avoided.
            adverse effects may result from larger doses
            toxicity is less predictable, depending on myocardial and serum potassium and calcium levels.

patients with cardiovascular shock have compromised renal perfusion
digoxin may result in high blood levels because it is excreted in the kidneys

High after load

Patients may have a increase in systemic vascular resistance
            resulting in high afterload
            poor peripheral perfusion.

afterload-reducing agents =, nitroprusside used in combination with dopamine.

pulmonary thermo-dilution catheter = measures cardiac index and to calculate systemic vascular resistance

intra-aortic balloon counter-pulsation
                        reduces afterload by mechanical means
                        increases diastolic coronary perfusion.

ECMO - extracorporeal membrane oxygenation is useful in reversible ventricular failure





sugf � s @�� (y� ardiac disease.
Assess pulse (central and peripheral) and capillary refill (assuming extremity is warm): <2 sec is normal, 2 to 5 sec is delayed, and >5 sec is markedly delayed, suggesting shock. Decreased or altered mental status may be a sign of inadequate perfusion.
Blood pressure (BP): Measuring blood pressure is one of the least sensitive measures of adequate circulation in children.
MANAGEMENT
Chest compressions
Fluid resuscitation
If peripheral intravenous (IV) access is not obtained in 90 sec or three attempts, and the patient is <8 years old, then place an intraosseous (IO) needle
If still unsuccessful, consider central venous access.
Initial fluid should be lactated Ringer’s (LR) or normal saline (NS).
Administer a bolus with 20 mL/kg over 5 to 15 minutes. Reassess. If there is no improvement, consider a repeat bolus with 20 mL/kg of the same fluid.

Reassess. If replacement requires more than 40 mL/kg, or if there is acute blood loss, consider 5% albumin, plasma, or packed red blood cells (RBCs) at 10 mL/kg.
If cardiogenic etiology is suspected, fluid resuscitation may worsen clinical status.
Pharmacotherapy: See inside front and back covers for guidelines for drugs to be considered in cardiac arrest.
Note: Consider early administration of antibiotics or corticosteroids if clinically indicated.

MANAGEMENT OF CIRCULATION
 Location *                                           Rate (per min) Compressions:   Ventilation
Infants                                       >100                                                    5:1
1 finger-breadth below intermammary line
Children (<8 yr)                                    100                                                      5:1
2 finger-breadths below intermammary line    
Older children                           100                                                      15:2
(>8 yr Lower half of sternum  
*Depth of compressions should be one third to one half anteroposterior (AP) diameter of the chest and should produce palpable pulses.

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